paediatrics Brussels 17

Ewing’s sarcoma family of tumours

• Although Ewing’s sarcoma most commonly is an undifferentiated tumor of bone, it may arise also from soft tissues (extraosseous Ewing’s sarcoma – EES)

• A more differentiated form of this entity, known as peripheral primitive neuroectodermal tumor (pPNET) , occurs as a primary tumor of bone or soft tissues

• Ewing’s sarcoma family of tumors (ESFT): a spectrum of a single neoplastic entity